Pseudoxanthoma elasticum: description of a late onset case.
نویسندگان
چکیده
Pseudoxanthoma elasticum (PXE) is a genetic multisystem disorder characterized by ectopic mineralization of connective tissues with primary manifestations in the skin, retina and cardiovascular system, and a phenotypic spectrum highly variable.This article presents the case of a 46-year-old male patient with sporadic late-onset PXE, without severe systemic complications.
منابع مشابه
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عنوان ژورنال:
- Indian journal of dermatology, venereology and leprology
دوره 76 4 شماره
صفحات -
تاریخ انتشار 2010